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KMID : 0363220130510050339
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Korean Journal of Dermatology
2013 Volume.51 No. 5 p.339 ~ p.342
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Congenital Melanocytic Nevus with Asymptomatic Neurocutaneous Melanosis
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Hong Soon-Kwon
Hwang Sung-Hwan
Kang Mi-Seon
Lee Young-Seok
Seo Jong-Keun
Kim Hyo-Jin
Lee Deborah
Sung Ho-Suk
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Abstract
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Congenital melanocytic nevi (CMN) are benign pigmented lesions that are defined as a tissue malformation of the neuroectoderm. Giant melanocytic nevi with multifocal involvement show significantly greater risk of developing malignant melanomas and neurocutaneous melanocytosis, particularly those in a posterior axial location. Neurocutaneous melanosis is a rare, congenital, non-inherited disorder characterized by the presence of large, multiple congenital melanocytic nevi with proliferation of melanocytes in the central nervous system. Asymptomatic neurocutaneous melanosis can be detectable only by MRI. The patients who have clinical manifestations have an extremely poor prognosis. We present a patient with giant congenital melanocytic nevi involving a major portion of the back with multiple satellite nevi scattered over the whole body associated with asymptomatic neurocutaneous melanosis. We emphasize the importance of imaging study for detection of early neurological symptoms or melanomas. To our knowledge, this is the first case of giant congenital melanocytic nevi associated with asymptomatic neurocutaneous melanosis in Korean dermatologic literatures.
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KEYWORD
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Congenital melanocytic nevus, Magnetic resonance imaging, Neurocutaneous melanosis
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